RAG2 and limb-girdle muscular dystrophy: In addition, dystrophic muscles from both murine models injected with DPPSC featured a higher frequency of fibres with larger cross-sectional area and reduced fibrosis and collagen content, expanding the previous report in Scid/mdx mice using DPSCs [28] also for the limb-girdle muscular dystrophy mouse model Sgcb-null Rag2-null γc-null.