These children had the following diagnoses: 18 had biliary atresia, 4 had cirrhosis, 4 had Alpha-1 antitrypsin deficiency, 2 had Alagille syndrome, 2 had familial intrahepatic cholestasis and 1 had glycogen storage disease Type IV. This evidence concerns the gene SERPINA1 and glycogen storage disease due to glycogen branching enzyme deficiency.