CBS, as a scarce clinical phenotype, is associated with its classical histopathology, CBD, but also with other proteinopathies related to tau, amyloid, and transactive response DNA-binding protein.2 Diagnostic criteria of CBS associated with CBD include rigidity or akinesia, dystonia or myoclonus of limb, cortical sensory deficit, alien limb phenomena, or orrobuccal/limb apraxia.1 Interestingly, the disease most often affects the hand.3 When considering a patient having probable CBS with the pathology of CBD, four of the mentioned symptoms should be present asymmetrically. Here, MAPT is linked to red-green color blindness.