FANCJ, originally designated BRCA1-interacting C-terminal helicase 1 (BACH1) (or BRCA1-interacting protein 1 (BRIP1)) for its interaction with the tumor suppressor BRCA1 [122], is genetically implicated in the progressive bone marrow failure disorder Fanconi Anemia (FA) [123,124,125]. The gene discussed is BRIP1; the disease is Fanconi anemia.