DMPK and Proximal myotonic myopathy: There are two main DMs forms: Myotonic dystrophy type 1 (DM1), which is the most common adult form of muscular dystrophy (due to a CTG-repeat expansion of at least 50 repeats in the non-coding 3' UTR of the myotonic dystrophy protein kinase(DMPK)-gene) [3], and Myotonic dystrophy type 2 (DM2), which is an autosomal dominant disorder caused by mutations in the zinc finger protein 9(ZNF9)-gene [4].