In addition, mislocalization of MuSK was reported in SOD1‐G93A ALS model mice (Vilmont et al, 2016), and a transgene that modestly increases MuSK expression in muscle from the embryonic stage delayed denervation at NMJs and improved motor function but failed to increase survival of ALS mice (Pérez‐García & Burden, 2012). Here, SOD1 is linked to amyotrophic lateral sclerosis.