Previous animal work has identified an increased expression of miR-206 over time in the ALS SOD1 G93A mouse model (Toivonen et al., 2014) and the murine spinal muscular atrophy model (Valsecchi et al., 2015), correlating with increasing pathology and associated muscle denervation. The gene discussed is SOD1; the disease is proximal spinal muscular atrophy.