Subsequently, more Drosophila models of HD and SCA3 (Steffan et al., 2001; Lee et al., 2004; Warrick et al., 2005; Kaltenbach et al., 2007; Li et al., 2008; Romero et al., 2008; Doumanis et al., 2009; Weiss et al., 2012), as well as other polyQ diseases, including SCA1 (Fernandez-Funez et al., 2000), SCA6 (Tsou et al., 2015, 2016), SCA7 (Jackson et al., 2005; Latouche et al., 2007), SCA17 (Ren et al., 2011), SBMA (Takeyama et al., 2002; Pandey et al., 2007; Nedelsky et al., 2010), and DRPLA (Nisoli et al., 2010; Napoletano et al., 2011) were developed. This evidence concerns the gene ATXN3 and Huntington disease.