The expression levels of complex I subunits NDUFA7, NDUFA10, NDUFB10, and NDUFB8 were significantly reduced (p ranging from <0.05 to <0.001) when compared with MA cases and using β-actin for protein normalization, expression of which was maintained in DLB and rpDLB when compared with MA cases. Here, NDUFB10 is linked to microtia.