FLCN and Fibrofolliculoma: Recently, the European BHDS consortium has proposed a set of criteria for the diagnosis of BHDS (Table 2).[70] Upon diagnosis of BHDS, the patients should undergo examination of the skin for fibrofolliculomas, CT imaging of the thorax for lung cysts, abdominal MR or CT imaging for renal tumors as well as genetic screening for pathogenic FLCN mutations.