Patients with transcription factor-linked MODY have different associated features based on their underlying aetiology, such as glycosuria in HNF1A-MODY, fetal macrosomia and neonatal hypoglycaemia in HNF4A-MODY, and developmental disorders of the kidney and multiple other organs in HNF1B-MODY (Fig. 2) [6]. Here, HNF1A is linked to MODY.