In addition to ABDs, nonepidermolytic ARCI occurs in the Jack Russell terrier due to a defective structural protein (transglutaminase 1, TGM1) [13] and in great Danes due to a defect in a fatty acid transporter protein (FATP4 aka SLC27A4) [19, 20]. This evidence concerns the gene TGM1 and autosomal recessive congenital ichthyosis.