Rare autosomal recessive mutations in the calcium‐sequestering protein, CASQ2 (2–5% of all cases), account for a small fraction of CPVT population (Lahat et al, 2001; Laitinen et al, 2001; Priori et al, 2001; Postma et al, 2002). Here, CASQ2 is linked to catecholaminergic polymorphic ventricular tachycardia.