As depicted in Table 3, the concordance between the primary RCC and its rhadboid/sarcomatoid component was seen in 2/3 cases: FGFR3 F386L and VHL1 V13fs*7 (rhabdoid and primary RCC) and VHL1 P97R and JAK3 (rhabdoid and sarcomatoid component of RCC). This evidence concerns the gene VHL and renal cell carcinoma.