Deletion of WT1 in the PHMP/PPFs continuum, i.e. in the G2+ domain, causes a phenotype characterized by defects in the inflow tract of the heart, coronary vessels (Cano et al., 2016) and, importantly, Bochdalek's hernia, most frequently located in the left side (Figure 2). This evidence concerns the gene WT1 and Posterolateral diaphragmatic hernia.