Although MAPT mutations, which account for 2–11% of all FTD cases [4], are mainly found in individuals with typical FTD, mutations in individuals with progressive supranuclear palsy (PSP), corticobasal degeneration (CBD), mild late-onset parkinsonism, and dementia with epilepsy, have also been identified [5]. This evidence concerns the gene MAPT and frontotemporal dementia.