FXN and Friedreich ataxia: Because sensory neurones are difficult to obtain and may not survive long-term in culture, in this study, we have used FRDA patient fibroblasts (GM03665, 445 and 740 GAA repeats) and fibroblasts of the YG8sR mouse model that carries 120 GAA repeats in intron 1 of a human FXN transgene to investigate correction of FRDA by lentivirus vectors (LVs).