COL6A1 mice, a COLVI null model (Bonaldo et al., 1998), and COL6A3 deficient mice (Pan et al., 2013) develop a mild myopathy and tendon dysfunction possibly due to altered tendon fibrillogenesis (Izu et al., 2011; Pan et al., 2013). This evidence concerns the gene COL6A3 and myopathy.