Pathogenic variants of MYO7A, the human homologue of myosin VIIa, can cause Usher syndrome, the leading cause of deaf-blindness (Bonnet and El-Amraoui, 2012), as well as the non-syndromic forms of deafness DFNA11 (Liu et al., 1997) and DFNB2 (Weil et al., 1997). The gene discussed is MYO7A; the disease is deafness.