Overall, among the 101 patients from this cohort, 57 (56.5%) had typical LN or typical pauci-immune GN, without overlapping antibodies; 12 (12%) had typical LN and positive ANCA antibodies; 30 (29.5%) had typical pauci-immune GN and positive ANA antibodies; and only 2 (2%) patients fulfilled the classification criteria for both SLE and AAV, corresponding to the SLE/AAV overlap syndrome. Here, BTG3 is linked to ganglioneuroma.