Only a few reports of GATA3 expression in neoplastic cells have been published in patients with mesenchymal tumors.[7] A patient with biphasic synovial sarcoma showed sporadic GATA3 expression; in contrast, focal to extensive expression was observed in patients with myxofibrosarcoma, undifferentiated/unclassified sarcomas, poorly differentiated angiosarcoma, leiomyosarcoma, and malignant peripheral nerve sheath tumor. Here, GATA3 is linked to malignant peripheral nerve sheath tumor.