Syndromic forms of aniridia have been described, the best known of which is WAGR (Wilms tumor, aniridia, genital malformations, intellectual disability [retardation] [MIM: 194072]) resulting from a contiguous gene defect encompassing PAX6 and WT1 (MIM: 607102).9 This evidence concerns the gene WT1 and Nephroblastoma.