Histopathological examination of the resected small bowel tumour confirmed metastatic Ewing sarcoma, morphologically similar to the spinal tumour (Figs. 8 and 9).The entire panel of immunochemical stains including CD99, synaptophysin, chromogranin, MNF-116, AE1/AE3, epithelial membrane antigen (EMA), CD34, HMB-45,desmin and S100 showed similar results in both the vertebral as well as the small bowel tumour (Figs. 10, 11, 12 and 13). The gene discussed is PMEL; the disease is small intestine neoplasm.