Histopathological examination of the resected small bowel tumour confirmed metastatic Ewing sarcoma, morphologically similar to the spinal tumour (Figs. 8 and 9).The entire panel of immunochemical stains including CD99, synaptophysin, chromogranin, MNF-116, AE1/AE3, epithelial membrane antigen (EMA), CD34, HMB-45,desmin and S100 showed similar results in both the vertebral as well as the small bowel tumour (Figs. 10, 11, 12 and 13). Here, DES is linked to small intestine neoplasm.