Benign hereditary chorea is an autosomal‐dominant, nonprogressive infantile or childhood‐onset condition presenting with generalized chorea that usually diminishes or disappears with age,40 differing from ADCY5 mutations in which choreoathetosis is often initially episodic and progressively becomes constant.1, 3 Therefore, we propose that infantile‐onset chorea, with exacerbation during drowsiness or arousal, should alert the clinician to the possibility of an ADCY5 mutation. The gene discussed is ADCY5; the disease is Benign familial chorea.