In this study, 36.13% of our patients presented GJB2 mutations together with nonsyndromic SNHL, and more than half (53.85%, 63/117) of the nonsyndromic SNHL patients with an identified molecular etiology were diagnosed with homozygous or compound heterozygous mutations in GJB2. GJB2 c.235delC was the most common mutation identified, accounting for 59.68% of the mutant GJB2 alleles, which is comparable to the results of earlier studies [1]. The gene discussed is GJB2; the disease is sensorineural hearing loss disorder.