More than ten different clinical syndromes have been attributed to LMNA mutations like FPLD 2, congenital muscular dystrophy, dilated cardiomyopathy type 1A [2] The wide phenotypic heterogeneity of diseases resulting from a mutation in a single gene may be explained by the variable roles of the nuclear lamina [2]. Here, LMNA is linked to dilated cardiomyopathy 1A.