The LQT type 6 (LQT6) causal gene, KCNE2 encoding for the potassium voltage-gated channel subfamily E member 2 (KCNE2) protein,15 has been implicated in the development of inherited, acquired and sporadic forms of LQTS.13,16-18 This protein consists of an extracellular N-terminal, a transmembrane and intracellular C-terminal domain. This evidence concerns the gene KCNE2 and familial long QT syndrome.