NR2E3 and Atrophy: It is important to notice that this phenotype is milder than the one found in recessive forms [18] and to point that the fundus alterations (additionally to typical RP fundus, atypical findings are present as macular changes and choriocapillaris atrophy) and ERG findings (impaired photopic and flicker records in the first stages of the disease) observed in some of our patients, are not the classical RP changes previously described in the European and North American NR2E3 dominant patients [17, 19, 20].