Moreover, RP resulting from CRB1 mutations may be accompanied by specific fundus features: preservation of the para-arteriolar retinal pigment epithelium (PPRPE) and retinal telangiectasia with exudation (also referred to as coats-like vasculopathy) [4], which is a well-known, although rare, complication of RP [5]. The gene discussed is CRB1; the disease is retinitis pigmentosa 1.