UCHL1 and proximal spinal muscular atrophy: Although, levels of UCHL1 are increased in SMA patient fibroblasts (Supplementary Table 1; Hsu et al., 2010) and in mouse models (Powis et al., 2014; Wishart et al., 2014), our results indicate that UCHL1 occurs at lower levels in SMA motor neurons compared to control motor neurons.