Muscle specimens of patients with DPAGT1 myasthenia have shown prominent myopathic features, attributed to hypoglycosylation of multiple muscle fiber proteins, including fiber‐type disproportion, degenerating mitochondria, and destruction of the muscle fiber organelles associated with autophagy.34 Furthermore, unlike most other CMS subtypes, the DPAGT1 and GFPT1 myasthenia subtypes are associated with the appearance of tubular aggregates on muscle biopsy, and these inclusions were detected on muscle biopsy of all 4 patients with these subtypes in our study. Here, DPAGT1 is linked to Fatigable weakness.