Multiple osteomas of the jaws along with other pathologies like colorectal polyps with high malignity, cutaneous fibromas, congenital retinal pigment hypertrophies, and multiple impacted or supernumerary teeth, enostoses, or epidermal cysts, are characteristic findings in Gardner's syndrome (familial adenomatous polyposis) which is an autosomal dominant disease caused by a mutation in the APC (adenomatous polyposis coli) tumor suppressor gene [8, 15, 27]. Here, APC is linked to Familial adenomatous polyposis.