Upon further testing, induced hypoglycemia with 75% carbohydrate meal intake showed BG of 36 mg/dL three hours later, with inappropriately elevated C-peptide (7.8 ng/mL; normal [nr] <0.2 in hypoglycemia), proinsulin (11.5 pmol/L; nr: <5 pmol/L in hypoglycemia), and insulin levels (22.4 μIU/mL; nr < 3 in hypoglycemia), consistent with EHH. This evidence concerns the gene INS and Hypoglycemia.