It seems that the tumor is not arise in the kidney and perhaps originate from scattered neuroendocrine cells derived from acquired or congenital abnormalities, because no neuroendocrine cell was detected within the renal parenchyma or hilum [8] and renal carcinoid tumors showed absence of reactivity with PAX-2 and PAX-8 [9]. This evidence concerns the gene PAX8 and neoplasm.