BIRC5 and pulmonary arterial hypertension: Moreover, the rate of the coexistence of organ involvement in dermal survivin-positive SSc patients (62.5 %, 6/9) (three cases with interstitial pneumonia (IP), two cases with renal crisis (RC) and one case with coexisting RC and pulmonary artery hypertension (PAH)) was higher than that in dermal survivin-negative SSc patients (0 %, 0/5) (p = 0.028).