However, similar to WDLPS, desmoid-type fibromatosis usually presents as a discrete fibrous lesion within the soft tissues with long, sweeping fascicles of bland (myo)fibroblasts together with thin-walled, dilated vasculature and perivascular oedema and peripheral chronic inflammatory cell infiltration which cannot be found in MLL. This evidence concerns the gene KMT2A and desmoid tumor.