Cochlear implantation has been reported to offer satisfactory auditory performance to patients with severe to profound deafness caused by mutations in the GJB2 gene, the solute carrier family 26 member 4 gene (SLC26A4), the otoferlin gene (OTOF) [10], or the myosin XVa gene (MYO15A) [11]. This evidence concerns the gene OTOF and deafness.