Mutations in genes like pancreatic and duodenal homeobox 1 (PDX1, MODY4), hepatocyte nuclear factor 1 beta (HNF1B, MODY5) neurogenic differentiation 1 (NEUROD1, MODY6) and insulin (INS, MODY10) cause relatively rare forms of MODY (Naylor and Philipson, 2011). This evidence concerns the gene PDX1 and MODY.