Typical SCA17 presents with ataxia and cognitive decline.[3] However, some patients present with atypical symptoms such as a Huntington’s disease-like phenotype [4] and Parkinsonism.[5, 6] Even non ataxic features have been reported as well.[5, 7] It has been suggested that lower-ranging expansions of SCA17 are more likely to cause parkinsonism than ataxia.[8]. Here, TBP is linked to spinocerebellar ataxia type 17.