Incidence of nodular shadows (78 % in PR3-ANCA positive cases and 100 % in MPO-ANCA positive cases) and thickening of trachea or bronchial walls (56 % in PR3-ANCA positive cases and 67 % in MPO-ANCA positive cases) reported in this study is close to the results reported in the previous studies of GPA. The gene discussed is PRTN3; the disease is granulomatosis with polyangiitis.