VHL and hemangioblastoma: Hemangioblastoma is a benign tumour of uncertain histogenesis characterised by the presence of stromal cells and a rich vascular component.1 Most cases, which generally arise from the central nervous system (CNS), are sporadic, while approximately 25% are associated with von Hippel-Lindau (VHL) disease, an autosomal dominant disorder associated with germline mutations in the VHL tumour suppressor gene located on the short arm of chromosome 3.2, 3