After the pathological diagnosis, on suspicion of an associated autoimmune disease, autoantibodies were examined and were positive for antinuclear antibodies (speckled type, ×640), rheumatic factor (114; normal range <15 IU/mL), and anti-SSA/Ro antibodies (>240; normal <10 U/mL) and negative for anti-SS-B/La, anti-DNA, anti-RNP, anti-Sm, anti-cyclic citrullinated peptide, Jo-1, Scl-70, and anti-neutrophil cytoplasmic antibodies (MPO-ANCA and PR3-ANCA). Here, CALR is linked to autoimmune disease.