So far, they include: (1) fused in sarcoma (FUS), TAR DNA-binding protein 43 (TDP-43), EWSR1 and TAF15, involved in amyotrophic lateral sclerosis (ALS) and/or some forms of frontotemporal lobar degeneration (FTLD) [39–42], (2) hnRNPA2B1 and hnRNPA1, linked to familial inclusion body myopathy with Paget’s disease of bone, frontotemporal dementia and ALS [43] and (3) TIA1, a protein associated with Welander distal myopathy [44]. This evidence concerns the gene HNRNPA2B1 and frontotemporal dementia.