In MPI-CDG (=CDG-Ib) (phosphomannose isomerase deficiency), the protein-losing enteropathy and hypoglycaemia can be treated with an oral uptake of mannose [22], in SLC35C1-CDG (=CDG-IIc), the leukocyte adhesion deficiency can be treated with oral fucose [23], and in PGM1 (Phosphoglucomutase 1 deficiency), treatment with galactose leads to improved indexes of glycosylation [24]. Here, MPI is linked to hyperinsulinemic hypoglycemia, familial, 4.