Thymic MALT lymphoma seems to be clinicopathologically a distinctive form with prevalence in Asians, strong association with autoimmune disease, marked female predominance, frequent presence of epithelium-lined cysts, almost invariable presence of a neoplastic plasma cell component, expression of IgA phenotype, and absence of API2-MALT1 gene fusion [68, 69]. This evidence concerns the gene BIRC3 and MALT lymphoma.