EYA4 and sensorineural hearing loss disorder: Mutations in the EYA4 gene cause inherited DFNA10 autosomal dominant hearing loss [9] and share a similar phenotype: postlingual onset, with the age of the first attack varying from 6 to 50 years old; progressive, sensorioneural hearing loss (SNHL) at first, with hearing loss in the middle frequencies and tinnitus as the most common complaints; and continued SNHL, with all frequencies become involved as age increases and the degree of hearing loss gradually evolving from mild to moderate and severe [17].