UQCC2 and hyperinsulinemic hypoglycemia, familial, 4: Sequencing the “MitoExome,” i.e., through the specific capture of both mtDNA and ∼1,000 nuclear genes encoding (part of) the mitochondrial proteome (Calvo et al., 2012), a mutation in UQCC2 (C6orf125; OMIM 614461) was discovered in a patient with profound CIII deficiency (Tucker et al., 2013).