This may be due to i) the fact that despite normalization of leukocyte counts, dysfunctional glucose-6-phosphatase deficient neutrophils are less effective in dealing with inflammatory processes [15], ii) the acute inflammatory stage of the IBD-like disease had already passed and a mainly scarring stenosis remained, when the patient presented as indicated by the scarred endoscopic and pathologic appearance. The gene discussed is G6PC1; the disease is inflammatory bowel disease.