Lynch syndrome, also known as hereditary nonpolyposis colorectal cancer (HNPCC), is an inherited cancer syndrome caused by defect in one of the mismatch repair (MMR) genes—MLH1, MSH2, MSH6 and PMS2. It accounts for about 5% of all colorectal and endometrial cancers diagnosed [1,2]. Here, PMS2 is linked to hereditary nonpolyposis colon cancer.