CCNE2 and disseminated peritoneal leiomyomatosis: We described 22 cases of TNKLPD with systemic presentation, including CAEBV of T/NK type and systemic EBV + T cell LPD of childhood and found the presence of a monomorphic infiltrate and high cyclin E2 and Ki-67 expression to be associated with poor outcome in TNKLPD, which is a rare disease with no known markers of prognostic significance to date.